Clinica de Ortodoncia Dr. Arthur Nouel

This malformation is very rare, since the first publication which was attributed Gaillard and Nogué to Antoine De Jussieu in 1718, to present time there have been less than 35 cases reported (Grinspan, 1976). This anomaly is almost always associated to malformations in the extremeties, especially the hands and feet, cleft palate and dental agenesia. Agglosia syndrome is in reality a microglossia with extreme glossoptosis. What is commonly observed is a rudimentary, small tongue that stretches and lengthens if we grab it with forceps. As a consequence of the lack of muscular stimulus between the alveolar arches, these do not develop transversely and and the mandible does not grow in an anterior direction, producing as a result a severe dentoskeletal malocclusion. This syndrome shows no predilection for sex and has no genetic implications. Its etiology must be searched for in some sort of fetal cell traumatism in the first few weeks of gestation. Neither language or swallowing are sensibly affected by this condition.