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| Te invitamos a visitar la sección de Cirugía Bucal,
con las técnicas quirúrgicas más comunes de la especialidad. |
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oral diseases
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Peutz-Jeghers Syndrome
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| 5
yr-old girl with pigmentation of the lips and the
soles of the feet |
| Peutz-Jeghers
syndrome is a familial, autosomic dominant condition
with high penetrance and variable expressivity.
It consists of the association of oral and
perioral melanic pigmentations in the form of multiple,
independent elements of dark brown color, sometimes
bluish, 2 to 3 mm in diameter and of intestinal polyps
many times manifesting once the patient reaches an
adult age. While
Jeghers says the spots are indispensable to the diagnosis,
cases have been described where polyposis occurs with
no pigmentation and pigmentation occurs with no polyposis.
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Copyright 2000.Arthur Nouel-Todos
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